Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.
Authors: Arturo G Rosales, Javier A Martinez, Julio C Ortiz-Cruz, Anabel M Garcia, Dalia I Murillo-Geraldo, Carlos A Garcia-Becerra
Background: Hepatic Hemangioma (HH) is described as the most prevalent benign hepatic tumor, and it is usually discovered incidentally as a symptomless mass of less than 3 cm. Kasabach-Merritt Syndrome (KMS) is described as a rare but severe complication of some vascular tumors. This syndrome presents as severe thrombocytopenia accompanied with a consumptive coagulopathy. Case presentation: A 35-year-old female, with a history of a hepatic tumor that was incidentally diagnosed with an ultrasound, later develops abdominal distention, petechiae and prominent hematomas that appear with minimal trauma. At the initial approach are found hematological data of microangiopathic anemia, thrombocytopenia and consumptive coagulopathy accompanied with the histopathological and imaging diagnosis of a Giant HH. Conclusion: Although, it is a very rare complication, the severity of this Syndrome requires a prompt diagnosis and treatment.
Keywords: Kasabach-Merritt Syndrome, Hepatic Hemangioma, Giant Hepatic Hemangioma, Thrombocytopenia, Disseminated Intravascular Coagulation, Case Report.
Authors
Correspondence to:
Carlos A Garcia-Becerra, Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico agbcarlos94@gmail.com
Publication history:
Received 20 May 2023
Revised 28 Sep 2023
Accepted 06 Oct 2023
Published online 11 Jan 2024
Published in print 07 Mar 2024
Rosales AG, Martinez JA, Ortiz-Cruz JC, Garcia AM, Murillo-Geraldo DI, Garcia-Becerra CA. Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. EJMCR. 2023; 7(7): 137-139. doi:
10.24911/ejmcr/173-1684550572
Rosales AG, Martinez JA, Ortiz-Cruz JC, Garcia AM, Murillo-Geraldo DI, Garcia-Becerra CA. Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. https://www.ejmcr.com/?mno=153950 [Access: May 15, 2024]. doi:
10.24911/ejmcr/173-1684550572
Rosales AG, Martinez JA, Ortiz-Cruz JC, Garcia AM, Murillo-Geraldo DI, Garcia-Becerra CA. Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. EJMCR. 2023; 7(7): 137-139. doi:
10.24911/ejmcr/173-1684550572
Rosales AG, Martinez JA, Ortiz-Cruz JC, Garcia AM, Murillo-Geraldo DI, Garcia-Becerra CA. Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. EJMCR. (2023), [cited May 15, 2024]; 7(7): 137-139. doi:
10.24911/ejmcr/173-1684550572
Rosales, A. G., Martinez, . J. A., Ortiz-Cruz, . J. C., Garcia, . A. M., Murillo-Geraldo, . D. I. & Garcia-Becerra, . C. A. (2023) Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. EJMCR, 7 (7), 137-139. doi:
10.24911/ejmcr/173-1684550572
Rosales, Arturo G., Javier A. Martinez, Julio C. Ortiz-Cruz, Anabel M. Garcia, Dalia I. Murillo-Geraldo, and Carlos A. Garcia-Becerra. 2023. Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. European Journal of Medical Case Reports, 7 (7), 137-139. doi:
10.24911/ejmcr/173-1684550572
Rosales, Arturo G., Javier A. Martinez, Julio C. Ortiz-Cruz, Anabel M. Garcia, Dalia I. Murillo-Geraldo, and Carlos A. Garcia-Becerra. "Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.." European Journal of Medical Case Reports 7 (2023), 137-139. doi:
10.24911/ejmcr/173-1684550572
Rosales, Arturo G., Javier A. Martinez, Julio C. Ortiz-Cruz, Anabel M. Garcia, Dalia I. Murillo-Geraldo, and Carlos A. Garcia-Becerra. "Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.." European Journal of Medical Case Reports 7.7 (2023), 137-139. Print. doi:
10.24911/ejmcr/173-1684550572
Rosales, A. G., Martinez, . J. A., Ortiz-Cruz, . J. C., Garcia, . A. M., Murillo-Geraldo, . D. I. & Garcia-Becerra, . C. A. (2023) Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.. European Journal of Medical Case Reports, 7 (7), 137-139. doi:
10.24911/ejmcr/173-1684550572